Amyotrophic lateral sclerosis

Chimwe chezvirwere zvisingawanzoiti uye chinotyisa ndeye amyotrophic lateral sclerosis. Ichi chirwere chinokonzera kuora mitezo yemasumbu akawanda emuviri womunhu, asi chizivo chinoramba chiri pachena. Muenzaniso unonyanya kuzivikanwa ndeye mukurumbira wemasayendisiti anozivikanwa Stephen Hawking, iyo iyo nyaya inoshamisa, sezvo amyotrophic sclerosis inowanzoisa kurufu mukati memakore mashanu, uye Hawking akakwanisa kugadzirisa mamiriro kwenguva yakareba.

Zvimwe zviratidzo zveamyotrophic lateral sclerosis

Kusvika iye zvino, masayendisiti haana kukwanisa kugadzirisa zvikonzero zvinokonzera amyotrophic lateral sclerosis. Vamwe vanofunga kuti chirwere ichi chinotora nhaka, vamwe-viral. Pamusana pekuti ALS inowanikwa munenge vanhu vanenge 3 kusvika kune 10 000 uye inofambira mberi nokukurumidza, kuongorora zviratidzo kunenge kwakaoma. Pane uchapupu hwokuti amyotrophic lateral sclerosis inobva mumagumo ega, asi pane imwe neimwe zvikonzero zvechirwere zvinogona kunge zvakasiyana uye kwete nguva dzose.

Chirwere chacho hachigoni kugadziriswa nekuongorora kukuru, saka computed tomography munyaya iyi haisi kupa chigumisiro. Kuongororwa kwe amyotrophic lateral sclerosis kunobva pakuongorora kwakakura kwemasero e-cerebral cortex uye iyo yese ye cerebrospinal cord. Nenzira iyi chirwere chinogona kuonekwa uye chakasiyana kubva kune zvimwe zvipembenene zvepakati penheyo system ine zviratidzo zvakafanana.

Mune matanho okutanga, ALS inowedzera kusingazivikanwi, inogona kuratidzirwa chete nekushaya simba kwemakumbo uye kuvhiringidzwa kwekutaura. Nokufamba kwenguva, zviratidzo zvinowedzera kudarika:

Ikokupedzisira kuongororwa kunoitwa mushure mokunge zviratidzo zvisingazivikanwi zvekukundwa kwepakati nepakati pemakona emhepo mumurwere zvakagadziriswa. Izvi zvinoreva kuti kushandiswa kwekuparadzwa kwemakumbo emotokari kwakatanga uye munguva pfupi kuzadzisa kupera simba kuchaitika. Kazhinji kusvikira panguva ino, varwere havasi kurarama, sezvo rufu hunovapo semugumisiro wekuoma mukupemesa basa nekuda kwekurohwa kwemazamu anoenderana.

Kurapa kweamyotrophic lateral sclerosis

Sezvo pasina zvikonzero zvekusimudzirwa kwechirwere ichi, kurapwa kwayo hakusi kushanda. Iwe unogona kuderedza purogiramu yacho zvishomanana, uchishandisa chirongwa chinotsigira kuti uite kuti zviratidzo zvayo zvivepo. Chokutanga pane zvose zvinosanganisira kuputika kwemaapapu. Iyi nzira inoshandiswa kushandiswa muWest uye inobvumira kuwedzera hupenyu hwomurwere kwemakore mashanu kusvika ku10. Munyika yekare yeCIS, nzira iyi haisati yashandiswa nekuda kwemari yakakura yemidziyo.

Pane mushonga umwe chete unogona kuderedza kufambira mberi kwechirwere. Uyu Riluzol, unosanganisira rilutec. Inogumisa kuburitsa kweguramamate yemurwere nemuviri, semugumisiro wekuti kukanganisa kwemagetsi emhepo kunowedzera kudarika. Riluzole yakatangwa mukushandiswa kubva muna 1995 muU.S. uye nyika dzakawanda muEurope, asi ichi chiremba hachina kunyorwa uye hachishandisi.

Kunyangwe iwe wakakwanisa kuwana mushonga, usatarisira kuti zvichabatsira zvikuru chirwere chechirwere chacho. Paavhareji, Riluzole therapy inobvisa kudiwa kwekubatanidza ventilator kweinenge mwedzi.