Mhando dzose dzezvirwere zveropa (hemorrhagic) inowanzoitika mukurapa kwemazuva ano. Inenge 50% yezviitiko ndeye thrombocytopenic purpura, izvo zvinokonzera izvo zvakawanda uye hazvina kufanana. Ichi chirwere chinokanganisa mutumbi chero ipi zvayo.
Thrombocytopenic purpura - zvikonzero
Verlhof chirwere kana thrombocytopenic purpura, izvo zvinokonzera izvo zvisingazivikanwi kusvikira zvino - chiitiko chinowanikwa nemusayendisiti weGermany kare muna 1735. Muvanhu inonzi "chirwere chemavara" nokuti mune vakadaro vakadai vari pamusoro pemuviri pano uye apo vanoita zviratidzo zvakasiyana-siyana.
Zvirwere, muhuwandu hwezviitiko, zvinowanikwa muvana kubvira pakuberekwa kusvika pakuyaruka, uye zvino zvinokwanisa kupera zvachose kunyange pasina matanho ekurapa. Muvana vasati vava nemakore maviri, zviitiko zve purpura zvinowanzonyorwa nevakomana. Mukukura, izvi zvinowanikwa kune 1-13 varwere kunze kwevanhu 100 000, uye vazhinji vacho vane mhosva vari vakadzi.
Fomu dze thrombocytopenic purpura
Chirwere cheropa chinonzi thrombocytopenic purpura (chirwere cheVerlhof) chinoitika apo masero eropa-maplatelet, anodzingwa nemaune immune system uye kufa nguva isati yamboitika. Nguva yeupenyu hwavo panzvimbo yemazuva 7-10, maawa akawanda. Nokuda kwekugadzirwa kwemagetsi ehurumende, spleen inobata. Chirwere ichi chine maitiro akasiyana-siyana anoenderana nechinokonzera chirwere, asi akasiyana zvishoma muzviratidzo zvechiratidzo:
- autoimmune kana idiopathic;
- heteroimmune;
- transimmune.
Mafomu e-thrombocytopenic idiopathic purpura, pasinei nezvikonzero, anogoverwa mu:
- rinopinza;
- Isingagumi (uye kazhinji, kazhinji kana kuti inoramba ichidzoka).
Autoimmune thrombocytopenic purpura
Mune zvimwe zviitiko, mutumbi unotanga kurwisana pachako. Iyi ndiyo mhando dzakasiyana-siyana dzechirwere ichi. Platelets inoparadzwa nemusununguko wemuviri, unozviona semasero ekune dzimwe nyika. Iro rudzi rwechirwere dzimwe nguva runopesana nechekuita kweimwe nzira inogadzirisa muviri mumutumbi. Idiopathic thrombocytopenic purpura inozivikanwa nekuparadzwa kweplateletlet yayo pasi pesimba rezviitiko zvakawanda. Dzimwe nguva izvi zvinotapurirana maitiro, asi mumatambudziko akawanda zvikonzero zvinoita kuti chirwere chiitike ndezvizvi:
- systemic lupus erythematosus ;
- autoimmune hemolytic anemia ;
- allergenic vasculitis ;
- chronic lymphocytic leukemia;
- utsinye hepatitis;
- glomerulonephritis .
Heteroimmune thrombocytopenic purpura
Muhuduku, heteroimmune (isina-immune) version yechirwere ichi ndicho thrombotic thrombocytopenic purpura, inowanzoitika kakawanda kupfuura yevakuru. Nhau dzakanaka ndeyokuti vana vanofananidzira kuti vadzore zvakanaka. Zvinokonzera chirwere ndezvi:
- kutora mamwe madhiragi (paracetamol, furosemide, quinine, ampicillin, cephalosporins, betta-blockers, nezvimwe);
- vaconisation (vaccination with BCG, rinoputika, chibhokisi, influenza, poliomyelitis);
- zvirwere zvinotapukira.
Thrombocytopenic purpura - zviratidzo
Chirwere cheVerlhof, zviratidzo zvaro zvakanyatsonaka, zvakasiyana nenguva yekuonekwa kwechirwere. Iko ndiko kuti, pakutanga, mavanga kana, sezvavanonyatsodanwa navanachiremba-petechiae, zvinoratidzwa zvakanyatsojeka, zvishoma nezvishoma zvinoderedza kuwanda kwemavara uye zvinoshanduka kuva cyanotic, green hue, zvishoma nezvishoma kutendeuka. Pane imwe nguva nenguva, marudzi ose emakumbo anogona kuva pamuviri, iyo inotyisa, asi haisi kurwadziwa, kusiyana nekukuvadzwa kwekutambudzika kunobva mumunhu ane utano.
Kuvhunduka kunowanikwa zvikuru pamakumbo, kashoma pamuviri, uye kazhinji kasingaoneki, asi mucous ndeyezvimwe. Thrombocytopenic purpura ine zviratidzo zvakafanana kune vanhu vakasiyana. Vanogona kusimuka semubairo we microtrauma, uye pasina chikonzero. Chaizvoizvo, hemorrhage inoitika usiku. Muchiitiko ichi, murwere haanzwi kurwadziwa, kunze kwekushaya ropa, kana murwere achida kukurumidza kupinda muchipatara. Kusiyanisa:
- kubuda ropa mucous (kubva mumhino, gums, chibereko);
- mukati mekubuda ropa (muviri, renal, ophthalmic, cerebral).
Kuongororwa kwe thrombocytopenic purpura
Verlhof chirwere, kuongororwa kwemweya hakugone nekuonekwa kwezviratidzo, kunobva pamigumisiro yeongororo yeongororo yevarwere uye chiremba chekuongorora. Vanachiremba vanoita annesnesis apo thrombocytopenic purpura yakazviratidza iyo yekutanga. Mushure mokunge zvirwere zvinogadziriswa zvinowanikwa uye zviratidzo zvakasiyana-siyana zvinoitwa kubva pakutora ropa kuongororwa, vasati vaita kubuda ropa. Izvi zvinosanganisira:
- Cuff inotarisa, kana mukombe wekumanikidzirwa kuiswa kunoiswa maminetsi gumi. Kana pamagumo ewa nguva ino madhayisa ane ropa akaumbwa pasi peikombe, muedzo wacho wakanaka. Inoitwa muvana kubva pamakore matatu.
- Muedzo unosungirirwa apo chirwere chekurapa chinoshandiswa kune ruoko, iyo inopera nguva inopa marwadzo - iyi nzira yakakodzera kuvarwere vakuru.
Thrombocytopenic purpura, inosanganisira mitezo yechiratidzo icharatidza mufananidzo wakavimbika weropa remurwere. Izvi zvinosanganisira kuongerwa ropa kwe:
- hemoglobin;
- ropa clotting speed;
- chiyero cheplatelet;
- kusavapo kana kuvapo kwekudzorera kweropa clot;
- kuvapo kwema antiplatelets muropa.
Mukuwedzera, mumatambudziko akaoma kana nekusavimbika kune mamwe maitiro ekuongororwa kwe thrombocytopenic purpura, bone marrow biopsy inoitwa - trepanabiopsy. Nekubatsirwa kwechinhu chakakosha chetpanpan, chiduku chiduku chemupenya chinoitwa munharaunda yechiparari kutora zvishoma zvemafupa, periosteum uye cerebrospinal fluid kuti iongororwe.
Thrombocytopenic purpura - kurapwa
Zvirwere zveRopa zvinoda hutariro hwakakomba, nokuti hutano hwomurwere pane imwe nguva hunoenderana nehukuru pane izvi. Kurapa kwe thrombocytopenic purpura kunoitwa zvose muchipatara (panguva yechikamu chekuwedzera) uye kumba. Izvo zvinosungirwa kupa murwere kuzorora zvakakwana uye mubhedha wezororo kuti aderedze nhamba yezvinotyisa nguva. Mukurwisana nemamiriro ezvinhu aya, tsika dzechirongwa zvemishonga dzinoshandiswa pamwe chete nemishonga yevanhu. Zvakakosha kuti titevere kune imwe kudya.
Kuporesa chirwere cheVerlhof?
Zvichienderana nezera ripi uye panguva ipi iyo chirwere cheVerlhof chakaonekwa, pachava nemubvunzo wekugadzikana kwawo. Muhuduku, huwandu hwehutano hwakanaka huripo, kana mwana akaonekwa kuti akakurumidza uye akakwanisa kukunda mumwedzi mitanhatu. Mushure mekunge nguva iyi, kuongororwa kunova kusingaperi, uye zvinonzwika sehumorrhagic thrombocytopenia.
Vanhu vakuru havana ruzivo - ichi chiitiko chinogona kuvafambisa muupenyu hwavo hwose nekudimbu kwekuregererwa uye kuwedzera. Mune zvimwe zviitiko, chirwere chisingagumi chinonzi thrombocytopenic purpura chinogona kupora kana chirwere chacho chabviswa, kunyange izvi zvisingavimbisi 100%. Iri nhengo inoparadza maplatelet uye iyo muvengi wemuviri. Nzira yacho inoshandiswa seyekupedzisira kugadzirisa, apo mamwe maitiro ekurapa akanga asingabatsiri. Shandisa senzira yekugadzirira, uye nekubatsira kwe laparoscopy.
Thrombocytopenic purpura - zvinodhaka
Chinangwa chekurapa kwaVerlhof chirwere ndechekuchengetedza huwandu hweplatelets muropa pane imwe yero inoda. Idiopathic thrombocytopenic purpura inobatwa, muzviitiko zvakawanda kubudirira, iyo inobvumira kugadziriswa kwakasimba kwemakore mazhinji. Kana kana kurapwa kana chirwere chisina kubatsira, chirongwa chekutora mishonga chinoshandurwa kuva itsva. Kuti uite izvi, shandisa:
- Prednisolone (Methylprednisolone) inonzi steroid hormone-ine zvinodhaka, kuti kuderedze basa rekudzivirira muviri. Inoshandiswa mumatanho ekutanga ekurapwa, kusati kwabviswa chirwere.
- Interferon a2 inoshandiswa kupedza zvirwere zvayo, apo steroid mishonga haina simba.
- Immunoglobulin G inoshandiswa mushure mekuvhiyiwa kuti kuwedzere huwandu hweplatelet.
- Immunosuppressants (Cyclophosphamide, Vincristine uye Azathioprin) inoshandiswa apo murwere asinganzwisisi imwe kurapwa. Iko kunodzivirira kwezvirwere muropa, zvichiita kuti kuwedzerwa kwenhamba yemaplatelet.
- Mushonga weDanazol, kukurudzira chirwere chepituitary nekutambira kwenguva yakareba zvakanaka kunobata mufananidzo weropa.
Thrombocytopenic purpura - kurapwa nemishonga yevanhu
Izvozvo zvakanyanya thrombocytopenic purpura chirwere cheropa, uye naizvozvo mishonga yemishonga yemakwenzi (decoctions) ne hemostatic properties yakabudirira kushandiswa pakurapa kwayo:
- dioecious nettle;
- ropa-nehuro;
- coral bark;
- chokeberry;
- chikwama chomufudzi;
- chamomile;
- yarrow.
Kudya ne thrombocytopenic purpura
Hapana zvokudya zvakakosha zverwere rwaVerlhof. Zvakakosha kuti ndiro idzi dzinoshandiswa mune fomu inotonhora kana inotonhorera. Miti yemichero ne thrombocytopenic purpura, semichero inobatsira zvikuru asi haifaniri kukonzera kurwara. Nhamba yezvakataurwa zvinowanikwa:
- porridge - buckwheat, corn, oatmeal;
- michero nemiriwo mumhando yejisi - karoti, apuro, beet, pomegranate, tomato;
- mahonji - currants, macheri, raspberries;
- seafood;
- nyama - nyama yemombe.
Zvakakosha kubvisa kubva pakudya:
- salted products;
- tsvina;
- zvinonhuwira nemiti inonhuwira;
- muto wakaoma;
- zvinokurumidza-zvokudya zvinowanikwa;
- carbonated drinks;
- kofi;
- doro.
Thrombocytopenic purpura - zvinetso
Chirwere cheVerlhof, uyo ane matambudziko akaipisisa, zvinoda kutarisirwa kwakakwana kweutano. Zvinetso zvinosanganisira:
- cerebral hemorrhage;
- gastric and renal bleeding;
- Kuenda kumwedzi kwakanyanya kubuda muhucheche.
Thrombocytopenic purpura - kudzivirira
Apo murwere anowanikwa ane "thrombocytopenic purpura," izvi zvinoreva kuti kune hutano hwako mumwe munhu anofanira kusiya tsika dzakawanda, zvose zvinokuvadza uye zvakajairika, mararamiro ehupenyu. Matanho ekudzivirira anonongedza kuchengetedza huwandu hweplatelet ne hemoglobin nekuda kwekudya kwakapfuma, pamwe nekuregererwa kwezvinhu izvi zvinotyisa:
- kushambira;
- mitambo yakasimba;
- kudya kwakakomba kunorema kurasikirwa;
- zvinodzvinyirira mamiriro ezvinhu.