Huru yeArtharhar yakatumidzwa nezita rechiremba weAmerica uyo akatanga kurondedzera iyo pakati pezana remakore rapfuura. Kubvira panguva iyo ruzivo pamusoro pehutachiona urwu rwakawedzerwa zvishoma nekuda kwekushaikwa kwayo uye kuoma kwekudzidza, asi kuburikidza nemichina yemazuva ano haisi kungoonekwa chete muUtero, asiwo inobatwa zvakanaka.
Goldenhar syndrome - chii ichocho?
Iyo chirwere chinofungidzirwa, icho chiri mune zvezvechiremba chinonziwo "oculo-auriculo-vertebral dysplasia", "hemifacial microsomy syndrome", chirwere chepenemenhe ine nhamba yakawanda yekufananidza anomalies. Pathology inobatanidza nekukuvadza panguva yekukura kwekumbryonic yemagill arches - maitiro echitenderera anonzi cartilaginous, kubva pane iyo tambo pasi, temporomandibular uye sangano rekubatsira kunzwa zvinowanzoumbwa.
Kudzidza nekunyatsorondedzera chirwere cheHorldhar, chirwere chei, chiri chikonzero chekuoneka kwayo, masayendisiti akawana kuti vakadzi havagoni kutarisana nehutachiona ichi, uye kuburikidza nehuwandu hwahwo hunenge huri munzvimbo yechitatu pakati pezvikanganiso zve cranio-maxillofacial zone kukura mushure mekunge kukanganisa se "hare lip " Uye" mhumhi muromo ". Kuzivikanwa kwechirwere mu fetus kunokwanisika pamusi we20-24 wekubata kwechirwere kuburikidza ne-ultrasound diagnostic ne scanning mumatatu matatu.
Goldenhar syndrome - zvinokonzera
Hazvisi yakanyatsozivikanwa kuti chii chinonzi Goldenhar syndrome, asi masayendisiti akawanda anobata maonero pamusoro pehupenyu hwechirwere ichi. Zvikamu zvechirwere ndezvechimiro chisina kujairika, asi kakawanda mushure mekubvunza kwehama dzevarwere hutano hunenge hunoonekwa. Dzimwe dzidziso dzinofunga nezvehukama hwekuvandudzwa kwehutano nehuwandu mumatanho ekutanga ekudzivirira kwevamwe makemikari, mavhapiramu epachirwere.
Mukuwedzera, chokwadi chinotevera kubva kune an anamnesis chemukadzi ane pamuviri chinotaridzirwa kuti chinogona kukonzerwa nechirwere chekurwara:
- kuroora ropa;
- previous abortions ;
- kuwandisa muviri zvakanyanya;
- chirwere cheshuga.
Goldenhar syndrome - zviratidzo
Chirwere cheGoldengen chinowanikwa muchecheche pavanenge vachiona kuongorora, kazhinji kunoratidzwa nekuoma kwezviratidzo zvakadaro:
- kusvibiswa kwemajaya ezasi;
- kusakanganisika kuumbwa kweziso (kukanganisa kwechikonzero chemhirizhonga uye hukuru hwayo);
- deformation of the auricle;
- kukanganisa kukura kwekervical vertebrae.
Muzviitiko zvakawanda, zviratidzo zvinowanikwa kune rumwe rutivi rwechiso uye rutsi, zvipembenene zviviri zvepakati hazvina kufanana. Kuwedzerwa kwekuoma uye kusanganiswa kwezviratidzo kune mumwe nomumwe. Mukuwedzera kune izvi, pane zviratidzo zvinotevera zvinoshamisa zve Goldenhar syndrome:
1. Zvikamu zvechimiro chechiso nemuromo:
- chiso chinonzi asymmetry;
- kudzivirirwa kwezygomatic;
- rinoputika pamusoro;
- muromo wakafara;
- mamwe mabhanhire;
- mutauro anomalies;
- cleft palate kana muromo.
2. Zvikanganiso zvenhengo dzekunzwa nekuona:
- kushayikwa kwechikoro;
- aplasia ye canal auditory;
- matsi;
- strabismus;
- chirema che oculomotor musculature;
- eye cyst;
- atrophy of the iris;
- bulging eye.
3. Pathology yenhengo dzomukati uye skeletal system:
- chiremera chemukati wekunamatira pamwoyo;
- aorta shoma;
- tetrad of nhema ;
- anomalies ye bronchopulmonary system;
- hydrocephalus;
- deformation of the renal pelvis;
- kukanganiswa kwemakwenzi;
- clubfoot;
- kusanganiswa kwekutanga kwechibereki vertebra nemaspipital bone;
- scoliosis;
- pfungwa isina kusimba.
Goldenhar syndrome - kurapwa
Mukubatana kwezviratidzo zve multicharacteristic, varwere vane Goldenhar syndrome vanofanirwa kusiyanisa kurapwa, iyo inowanzoitwa mumatanho akawanda, apo mwana anokura. Muzviitiko zvinyoro, zvinokwanisika kuchengeta nyanzvi dzakasiyana kusvikira mwana asvika pamakore matatu, mushure mokunge maitiro ekurapa anokurudzirwa, kusanganisira chirongwa chekuvhiya, chirwere chinonzi orthodontic therapy. Mumatambudziko akaoma, akawanda emitambo inoitwa kusvikira imwe yemakore kana maviri.
Mishonga ye orthodontics inoitwa muzvikamu zvitatu zvikuru, izvo zvinoenderana nekuvandudzika kwe dentoalveolar system (nguva yemukaka wemeno, nguva yekuchinja, nguva yekuruma nokusingaperi). Varwere vanopiwa zvibvisa zvinogadziriswa uye zvisingadziviriki zvekugadziriswa kwejaya uye kukanganisa kwemajeri, uye mazano anopiwa maererano nemitemo yekunyatsotarisirwa. Kazhinji nezera remakore gumi nemasere kusvika gumi nematanhatu, matanho ose ekurapa nekuvandudza ari kupera.
Goldenhar syndrome - operation
Gemifacial microsomia inobatwa nechisungo chekugadzirisa kwekupindira, rudzi, chiverengo uye nhamba yeiyo inopesana zvichienderana nehuwandu hwekukuvara. Kazhinji, idzi marudzi emabasa anotumirwa:
- endoprosthetics yenguva yechiromandibular, maraya (pasi, kumusoro);
- kushungurudza-kukanganisa osteosynthesis;
- osteotomy yemhino;
- osteotomy of jaws;
- genioplasty;
- rhinoplasty;
- plastiki yewaricle;
- mhirizhonga yakasara yejaya rezasi, nezvimwewo.
Vanhu vane Goldenhar syndrome
Varwere vanoonekwa kuti vane Goldenhar syndrome vasati vasvika uye pashure pokuvhiyiwa vanogona kutarisa zvakasiyana. Kana nguva yakakodzera muhuduku ichaitwa maitiro, kusanganisira plastiki, uye zviratidzo zvekunze zvechirwere zvinogona kunge zvisipo. Kune mienzaniso yakawanda apo vanhu vane Goldenhar syndrome vanobudirira kudzidza, kuwana basa rakanaka, kutungamirira mhuri uye kubereka vana.
Goldenhar syndrome - kufungidzira
Kune varwere vane Goldenhar syndrome, kufungidzira kunofadza mumatambudziko mazhinji, uye zvakawanda zvinoenderana nekuwanda kwekukuvadza kwemuviri. Nekuonekwa kwehutano hwakawanda hwekunakisa, kushandiswa kwezvose zvinogona nzira yekugadzirisa kukanganisa, kutarisa kwekutarisana pedyo nemurwere, kutsigirwa kwepfungwa, pane mukana wekugadzirisa zvakakwana.