Systemic scleroderma

Kushungurudzika mukuvandudzika kwezvibvumirano zvinokonzera kukanganisa kwayo uye zvimwe kuoma. Izvi zvinonzi systemic scleroderma uye inoratidzwa nekukundwa zvishoma nezvishoma nemidziyo midzi yeropa, epidermis, uyewo nhengo dzakawanda dzomukati.

Systemic scleroderma chirwere

Nokuda kwezvikonzero zvisingazivikanwi, vakadzi vanotambura kanomwe kazhinji kakawanda kupfuura varume vanorwara ichi, uye systemic scleroderma inowanzoitika mukukura.

Chirwere chacho chinoratidzwa nekukurumidza kupfurikidza nekugadzirisa kushandiswa kwemasumbu mumuviri, kubva paganda kusvika kune itsvo, moyo nemapapu.

Systemic scleroderma - zvinokonzera

Vamwe vanachiremba vanoratidza kuti chirwere ichi chinokonzerwa nemararamiro ekudzivirira uye genetic predisposition. Mukuwedzera kune zvinyorwa izvi, zvinotevera zvinokonzera ngozi zvinowanikwa:

Systemic scleroderma - zviratidzo

Kliniki yechirwere ine zviratidzo zvakadaro:

Systemic scleroderma - kuongororwa

Nemhaka yekufananidzwa kwezviratidzo zvinoratidzwa pamusoro apa nezvimwe zvirwere, zvinenge zvakaoma kuona chirwere, sezvo marudzi mazhinji ekutsvakurudza anodiwa. Chokutanga pane zvose, kutarisa kunotarirwa kune zviratidzo zvekunze - pallor yeganda, kushandurwa kwezviso zvemaziso (zvinoita sechigadziriswa mask nemiromo miduku), kuchena kwemaoko neminwe yakaoma uye phalanges yeminwe.

Uyezve, ruzivo rweruzivo rweropa runoshandiswa kuti ruzive zvirwere zvinopisa, immunogram, X-ray kuongororwa kwenhengo dzomukati kuti vaone chiyero chechirwere chavo, uye electrocardiogram.

Scleroderma systemic - kuraira

Pasina kugadzirisa zvikonzero zvinokonzera chirwere chacho, hazvikwanisi kurapwa, saka hutachiona hunogara husingaperi uye pakupedzisira hunotungamirira kukuremara kwemurwere.

Systemic scleroderma mune chimiro chakakomba chine kufungidzira kusina kunaka, chete nhamba shomanana yevarwere vanogona kurarama kwenguva refu kupfuura makore maviri. Nokurapa kwakakodzera, zvinokonzerwa kuderedza kufambira mberi kwechirwere zvishoma uye kuwedzera nguva iyi kusvika makore mashanu kusvika ku7.

Systemic scleroderma - kurapa uye nhungamiro itsva munharaunda iyi

Kuti kuderedza zviratidzo uye kuvandudza hupenyu hwehupenyu hwevanhu, nzira yakabatana yekurapa inoshandiswa:

Panguva ino, tsvakurudzo yakawanda uye kuedza stem cell transplantation pakugadzirisa kupera kwehutachiona. Mhedziso yekutanga yehutungamiri hutsva inoratidza kuti kurapa kwakadaro mune ramangwana kuchabatsira kusvika ku 95% varwere.

Systemic scleroderma - kurapwa nemishonga yevanhu

Mune mushonga unoshandiswa zvinoshandiswa kutora decoctions ye vasodilating herbs - hawthorn, St. John's wort, motherwort, oregano, burdock, clover uye calendula pane tei.

Mukuwedzera, compress inobatsira kugadzirisa marwadzo kubva patsva yakasimwa murosi weAloe, unofanirwa kushandiswa kune nzvimbo dzakapiwa zuva rega rega kwemaminitsi 20-30.