Hypertrophic cardiomyopathy

Chirwere ichi, chinowedzera rusvingo rwekuruboshwe, uye mune dzimwe nguva dzisinganzwisisiki ye ventricle yakarurama yemwoyo, inonzi hypertrophic cardiomyopathy (HCMC). Muchirwere ichi, kuwedzera mumatambudziko asinganzwisisiki kunoitika zvakasiyana, saka saka septum interventricular inowanzokuvara.

Zvinofungidzirwa kuti ichi chirwere chevatambi - ndezvekuwedzera kwekuita muviri kuti hypertrophy inowanikwa. Isati takaziva mamiriyoni emakwikwi apo vatambi vakafa pamitambo nemhaka ye hypertrophic cardiomyopathy - Hungarian mutevedzeri webhola Miklos Feher uye mutambi wenyika yeAmerica Jesse Marunde.

Muchirwere ichi, mishonga yemisumbu muyo marocardium ine nzvimbo yakashata, inosanganiswa nejen mutation.

Mafomu e hypertrophic cardiomyopathy

Nhasi, vanachiremba vanotaura zvitatu zve hypertrophic cardiomyopathy:

  1. Basal kudzivirira - chidimbu chekuzorora chinopfuura kupfuura kana chakaenzana ne 30 mm Hg. Art.
  2. Bhuku rekudzivirira - kuchinja kwemazuva ano kwema intraventricular gradient kunoonekwa.
  3. Kuvhiringidzika kwekupedzisira - chidimbu mumamiriro akadzikama pasi pe 30 mm Hg. Art.

Kubvisa hypertrophic cardiomyopathy inofananidzwa nemhando idzi zvitatu zvechirwere, asi chimiro chechokwadi chisina kudzivirira chinoratidzwa ne stenosis gradient pasi pe 30 mm Hg. Art. mumamiriro akadzikama uye anotsamwisa.

Zviratidzo zve hypertrophic cardiomyopathy

Zviratidzo zve hypertrophic cardiomyopathy zvingave zvisipo - vanenge 30 muzana vevarwere havaiti mhere-mhere, pane imwe nguva kufa kamwe kamwe kunogona kuve kuratidzwa chete kwechirwere. Munharaunda yakakonzerwa nengozi vaduku vaduku vasingaoni zvikwangwani, kunze kwekuvhiringidzika kwemwoyo.

Nokuti chirwere ichi chinoratidzirwa neinoti chediki-emission syndrome - munyaya iyi, kupera simba kunoitika, kuperevedza kwemhepo uye chizivo, uye kutina kutambudzwa kunoitika.

Uyezve, ne hypertrophic cardiomyopathy, pangave nekuratidzwa kwekusiya kuruviri rwemoyo kusakundikana, izvo zvinogona kukura kuva congestive moyo kusakundikana.

Kukundikana mumutambo wemwoyo kunogona kutungamirira pakupera simba . Kazhinji idzi idzi dzinonzi extraricstoles dzinobhururuka uye zvinokonzerwa ne ventricular tachycardia.

Muzvikamu zvisingawanzoitiki, varwere vanogona kuva nehutachiona hwekuputika uye thromboembolism.

Kuongororwa kwe hypertrophic cardiomyopathy

Kusiyana nedzimwe mhando dzehutachiona, hypertrophic fomu inoratidzika kuti yakanyanya nyore nekuda kwechikonzero chakagadziriswa: kuti chirwere chinogamuchirwa chibvumirwe, masicardial thickening inofanira kuva yakakura kupfuura kana yakaenzana na 1.5 cm pamwe nekuvapo kwechokusiya ventricular kudzvinyirira (kusagadzikana kusununguka).

Kana kuongororwa, murwere anowanikwa kuwedzera muganhu wemwoyo kuruboshwe, uye kana pavanodziviswa, ruzha runonzwika (systolic rhomboid).

Pakati pemamwe maitiro ekudzidza izvi zvirwere ndeizvi:

Kurapa kwe hypertrophic cardiomyopathy

Kuongororwa uye kurapwa kwe hypertrophic cardiomyopathy zvakabatana zvakanyanya kuti zvidzivirire kuparara. Mushure mokuongorora kuongororwa kwechikwata chechirwere, kana pane chiitiko chemugumisiro unouraya, zvakaoma kurapwa kunoitwa. Kana pasina rufu kune ngozi, uye zviratidzo hazviiti zvinoratidzwa, saka kurapa kwakanyanya hakuiti.

Kwokurapa zvakakosha zvikuru kupedza basa rekuita, uyewo kushandisa zvinodhaka neine ionotropic yakashata. Izvi zvinosanganisira beta-blockers uye vanopikisa calcium. Vanosarudzwa vari voga, uye vachipiwa kuti kugamuchirwa kunoitwa kwenguva yakareba (kusvika pakugashira kweupenyu hwose), nhasi vanachiremba vari kuedza kupa mishonga ine minda yakaipa. Pakutanga Anaprilin yakashandiswa, uye nhasi kune dzakafanana zvechizvarwa chitsva.

Uyewo, kurapa kwemasimba uye antibiotics inoshandiswa mukurapa kana zvichiitika kune chinotapukira chechirwere.