Hirschsprung chirwere chikamu chenguruve chemukati mudumbu. Murwere haaine masero emagetsi mumhepo inonzi plexus yeMeissner uye muscle plexus yeArabach. Pamusana pekusavapo kwezvimwe zvikamu munzvimbo yakakanganiswa uye kupera kwenguva refu kwechigaro mune mamwe madhipatimendi, pane kuwedzerwa kukuru nekuwedzerwa kwemukati.
Zviratidzo zveHirchsprung's disease
Zviratidzo zvekutanga zvechirwere cheHirschsprung ndezvekudzivirira, kuvimbiswa uye kuwedzerwa munharaunda yedumbu. Kana murwere asingabvunzi chiremba, zviratidzo zvekupedzisira zvinotanga kuonekwa. Izvi zvinosanganisira:
- anemia ;
- hypotrophy;
- fecal matombo.
Mune zvimwe zviitiko, varwere vanotambura marwadzo mudumbu, avo vane simba rinogona kuwedzerwa sezvo nguva yekuvharwa ichiwedzera.
Matanho eHirschsprung chirwere
Iyo syndrome yeHirschsprung inokura mumatanho akawanda. Chikamu chekutanga chechirwere chinobhadharwa: murwere ane kuvimbiswa, asi kwenguva yakareba, kucheneswa kwakasiyana-siyana kunobvisa nyore nyore.
Mushure meizvi, danho rinopedzerwa rinowanikwa, panguva iyo chirwere chacho chinowedzera uye chinowedzera kushanda. Panguva ino mukurudzirwa kwechirwere cheHirschsprung kuvanhu vakuru, kuwanda kwemuviri kunoderera, ivo vanotambudzika nekuremera mukati mamuviri nekupererwa kwemhepo. Mune zvimwe zviitiko, chirwere chakakomba chinokonzerwa nehutachiona uye chemagetsi chinowanikwa.
Chikamu chinotevera chechirwere chinoderedzwa. Varwere havasisina kubatsirwa nekuchenesa uye mavara akasiyana-siyana. Anenge achine manzwiro ekurwadza mumudumbu pasi, uyewo kubatwa kwepamu kunowedzera nokukurumidza.
Kuongororwa kwechirwere cheHirschsprung
Kana zvichikanganisika nezvechirwere cheHirschsprung, kuongorora kwemashure kunoitwa kutanga. Muchiripo chechirwere, ampoule isina chinhu ye rectum inowanikwa mumurwere. Inzwi re sphincter rinowedzera. Muchiitiko ichi, zvakakosha kuongorora shanduro yezvikamu zvose zvemuviri wepamuviri. Ne chirwere chaHirschsprung, mapundu emakoloni akawedzerwa uye anokonzerwa, dzimwe nguva achicherechedza mvura yemvura.
Murwere anotofanirawo kugamuchira sigmoidoscopy, irrigography, colonoscopy uye histochemical diagnostics.
Kurapa kwechirwere cheHirschsprung
Nzira chete yekurapa chirwere cheHirschsprung chirwere. Zvinangwa zvekushanda ndezvi:
- kubviswa kwematare ose akawedzerwa;
- kubviswa kwegangoniic zone;
- kuchengetedzwa kwechikamu chemuviri wakakura unoshanda.
Kune vana, shanduko dzeSwanson's, Duhamel's uye Soave dzakagadzirwa. Vanhu vakuru maitiro avo anowirirana zvinopesana nekuda kwezvinhu zvinotyisa uye zvakanyanya kuora mumutsipa kana kuti pamakumbo emumatumbo. Kazhinji kazhinji, neHirschsprung's disease, kushandiswa kwaDuhamel kunoshandurwa, umo nzvimbo yegangoni inodzingwa nekugadzirwa kwechidimbu chipfupi chese rectum. Muzviitiko zvakawanda, zvinogona kudzivirira kukanganisa kune sphincter ye anus uye kuumba airarectal anastomosis.
Asati avhiyiwa, murwere anoda
Kufanirwa kwehutachiona hweHirschsprung's disease mushure mekuvhiyiwa kunofadza. Asi mune dzimwe nguva, chirwere chinowanzoitwa chinogona kudiwa. Anenge nguva dzose chinangwa chekuvhiya kwakadaro kunoderedzwa kusvika pakuvandudzwa kwe anastomosis uye inoitwa kuburikidza ne peritoneal kana kupona kwese.