Cystic fibrosis chirwere chakakomba chinokanganisa zvirongwa zvose zvemuviri womunhu zvinounza maruva-kupumha, kudya, zvepabonde, glandira. Chirwere ichi chakajairika, asi kusvika munguva pfupi yapfuura, kupararira kwekurapa kwacho hakuna kukwezva. Cystic fibrosis varwere vanofanira kugamuchira mishonga yakanyatsosarudzwa munguva yavo yose, vachiongororwa nguva dzose uye vanobatwa nekusingaperi munguva dzekuwedzera.
Chikonzero uye maitiro e cystic fibrosis
Chikonzero chechirwere ndechekuchinjwa kwegene cystic fibrosis. Iyo jeni yakawanikwa chete makore makumi matatu yapfuura. Iko kuchinja kwegene iri kunotungamirira kukuti chakavanzika chakavanzwa nemasikironi chinowedzera kwazvo. Chakavanzika chakavanzika chinoputika mumasikirwe uye matukisi, anowedzera maitiro epachirwere-kanowanzoitwa Pseudomonas aeruginosa, Staphylococcus aureus, tsvimbo yehuputi. Somugumisiro, kupera kusingaperi kunowedzera.
Cystic fibrosis inowanikwa mumarudzi matatu:
- pulmonary;
- matumbo;
- kusanganiswa.
Zviratidzo zve cystic fibrosis muzvitsva
- Kuvhiringidzika kwepamuviri (mekonial ileus) - mumukati muduku kudyiwa kwemvura, sodium uye chlorine inoparadzaniswa, nokuti iyo yakavharwa meconium. Dumbu racho rinokurira mumwana, rinoputika ne bile, ganda rinova rakaoma uye rakasvibiswa, muitiro wevasipisi unowoneka pamubereki, mwana anova akasvibiswa uye asingashandi, zviratidzo zvekuzvidzivirira zvinopisa zvinoratidzwa nemhuru
- Nguva yakareba jaundice - inoratidzirwa muhafu yezviitiko zveeeconal ileus, asi inoshandawo sechiratidzo chekuzvidzivirira chechirwere. Iko kunokonzerwa nokuti bile inova yakaoma zvikuru uye inobudirira ichibuda kunze kwegungwa.
- Mwana wacho akaisa makristasi emunyu paganda rechiso uye mazamu, ganda rinova rinonaka.
Zviratidzo zve cystic fibrosis mucheche
Kazhinji kacho, cystic fibrosis inoratidzika apo mwana achisimudzirwa kune kudya kwakanyanyisa kana kuti injowa nezvokudya zvakakwana:
1. Chigaro chinova chakakomba, mafuta, zvakawanda uye zvinogumbura.
2. Chiropa chakawedzerwa.
3. Pangangodaro kuve nekuputika kweiyo rectum.
4. Mwana anorara shure mushure mekukura uye anoita zviratidzo zveDystrophy:
- ganda rinowoma uye rakasviba;
- inowedzera uye inoparadza mhinzwa;
- dumbu rinova guru uye rinoputika;
- Maoko nemakumbo zvakapfava ne phalanxes yeminwe nenzira ye "drumsticks."
5. Mucheche anoyamwa anotanga kuwedzera kwenguva refu kwete kupfuvura kuoma. Dense mucus inowedzera mubronchi uye inopesana nekufema kwemazuva ose. Muchikamu chinoramba chiripo, mabhakitiriya anowedzera nesimba, nekuda kwekuti pane purulent inflammation.
Vana vane cystic fibrosis vanofanira kugamuchira kurapa kwakakodzera. Iyo yakaoma yehutano hwekurapa inosanganisira:
- Antibacterial therapy - kurwisa utachiona muhutano hwemapfupa;
- mucolytic therapy - nokuda kwekunyangadza kwe sputum;
- kinesitherapi - kufema kunobatsira muviri;
- hepatoprotectors - nokuda kwechiquefaction ye bile;
- Vitamin therapy - kubhadhara kurasikirwa kwevhithamini nesheori.
Kuchengetwa kwevana vatsva kwe cystic fibrosis
Cystic fibrosis inogona kuongororwa semugumisiro wekuongororwa kwekliniki uye yebhroreta yemurwere. Kuti chirwere chacho chionekwe nekukurumidza, cystic fibrosis inowanikwa muurongwa hwekuongorora vana vekuzvarwa kwezvirwere zvekuzvarwa uye zvekuzvarwa.
Kubva kuongorora mwana achiri muchipatara kunotora sampu yeropa (kazhinji kacho kubva pasitsitsinho) ne "dope rakaderera" nzira. Izvi zvinoitwa musi wechina muvana vanoberekwa panguva kana musi wechinomwe muvana vasati vasvika. Muenzaniso weropa unoshandiswa kune chikwata chekuedza, ichocho zvino chinotungamirirwa nekudzidza mu laboratori. Kana paine kusafungirwa kwe cystic fibrosis, vabereki vanokurumidza kuziviswa pamusoro pekudiwa kwekuwedzera kuongororwa.